Vasculitis Table
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Transcript of Vasculitis Table
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7/25/2019 Vasculitis Table
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VASCULITISVasculitis C/F Bx/Micro Tx
LARGE-vessel: Aorta & its a!or "ra#c$es
Te%oralGia#t Cell'
Arteritis
F > M, >50yo
- Usually at branches of carotid artery- headache (temporal)- visual disturbances (ophthalmic)- ja claudication- polymyal!ia rheumatic ("u-li#e s$ % joint & muscle pain)
' (>*00)
+ranulomatous
n"amed vesselall % !iant cells& intimal brosis
(.i!h-dose)/orticosteroids
()IG) ris* o+"li#,#ess /otx..
Ta*aasuArteritis
01ulseless234'
dults 150yo(youn!, sian female)
- ortic arch at branch points- visual & neuro s$- ea# or absent pulse in upper e$tremity
'
+ranulomatous /orticosteroids
ME2IUM-vessel: i#volve uscular arteries t$at su%%l or5a#s
1olarterits#o,osa 1A6'
23 4U2+
6oun! adult
- .72 (renal artery)- abdom pain % melena (mesenteric artery)- neuro disturbances- s#in lesions
((((A/7: )BsA5((((
2eutrophils 8Fibrinoid 2ecrosis(F2)
0stri#5 o+%earls4 onima!in!
/orticosteroids/yclophosphame
F74 %o t$
8aasa*i 23
(M/ sian) #ids 19yo
:ects Coro#ar Arter..((- 7hrombosis Mneurysmupture
0CRAS) & "ur#4(2onspecic $)ConjunctivitsRash (des;uamatin!)Adenopathy (cervical)Straberry ton!ue)and-foot chan!es (edema, erythema)& Fever
IVIG 9 As%iri# F 90-B0yo
+ranulomas inC*) 23'C Dsaddle noseE (DC-shapedE depression of nose)) 2U'C Chronic sinusitisG) 4U2+C Cavitary !ranulomas9) ?@2'6C F2 +2
2eutrophils 8 F28 Gra#uloas
C-A6CA 1R'
4U2+, ?@2'6, ?2 % pauci-immune +2 & alpable urpura
- $%nf$
6?5ra#uloas..
2eutrophils 8 F2
1-A6CA M1?'9
/orticosteroids/yclophospham
e
elapses Icommon
C$ur5-Straussaller5ic
5ra#uloatosis & a#5iitis's#,roe
1A6 varia#t=@'
6oun! males
4U2+ & .'7
TRIA2:>' Gra#uloas@' Ast$a
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7/25/2019 Vasculitis Table
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- 1al%a"le 1ur%le 1ur%ura o# "uttoc*s/le5s- + pain & bleedin!- .ematuria (! nephropathy%Aer!er @J)- rthral!ias
severe