Tumores ósseos malignos
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Transcript of Tumores ósseos malignos
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TUMORES ÓSSEOS MALÍGNOS
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OSTEOSSARCOMAS
• Tu malígno primário do osso mais comum.
• Existem vários tipos de osteossarcomas
• Causa desconhecida.
• Fatores predisponentes:displasia fibrosa,Paget,radiação ionizante.
• Tipos medular,intra cortical e justa cortical.
• Existem tipos extra esqueléticos que atingem partes moles.
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• Ao forma clássica ocorre em adolescentes e adultos jovens,sendo o joelho o local mais comum.
• Ocorre geralmente na região metafisária de um osso longo quando a fise ainda esta aberta.Possui tendência a permanecer na metáfise,sem transpor a fise.
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RADIOLOGIA
• Destruição óssea cortical e medular com reação periosteal.
• Ocorre invasão das partes moles.• Radiopacidade inclui combinação de produção
de osso tumoral,matriz calcificada e osteóide.• Não se define a zona de separação da área
tumoral com o tecido preservado,indicando aspecto permeativo da lesão.
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• A reação peristeal pode configurar triângulo de Codman.
• A reação periosteal lamelar é a mais encontrada.
• De acordo com tipo histológico encontrado os osteossarcomas podem ser classificados em fibroblástico,osteoblástico,condroblástico e
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TIPOS
• Osteossarcoma convencional• Osteossarcoma central low grade• Osteossarcoma telangiectásico• Osteossarcoma de pequenas células• Osteossarcoma fibrohistiocítico• Osteossarcoma intra cortical• Osteossarcoma gnático(maxila ou mandíbula)• Osteossarcoma multi cêntrico• Osteossarcoma justa cortical• Osteossarcoma parosteal
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Pequenas células
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LOW GRADE CENTRAL
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LOW GRADE CENTRAL
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telangiectásico
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talangiectásico
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TELANGIECTÁSICO
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MULTI CÊNTRICO
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Multi cêntrico
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parosteal
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parosteal
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parosteal
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parosteal
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Osteossarcoma extra esquelético
• É um tu pouco comum do mesênquima.• Acomete pessoas da meia idade(pico 54ª)• Afeta extremidades inferiores• Pode atingir mama,tireóide,cápsula
renal,pulmão,próstata,bexiga.• Geralmente desenvolve pos radioterapia.• .geralmente aumento das partes moles sem
dor,com calcificações.• Pode invadir a cortical óssea.
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Extra ósseo
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Extra ósseo
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Causas de reação periosteal
• Fratura• Tu malígno primário do osso• Tu malígno secundário do osso• Osreomielite• Hemorragia sub periosteal• Granuloma eosinófilo• Artrite • Estase venosa• Hiperostose cortical infantil(CAFFEY)• Sífilis adquirida• Infarto ósseo• Cisto ósseo
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osteossarcoma
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Ewing
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Leucemia crônica
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Cisto ósseo
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Osteomielite crônica
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Reiter
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Estase vascular
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Caffey
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sífilis
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CASOS RÁPIDOS
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