Congenital Neurologic Disorders
Transcript of Congenital Neurologic Disorders
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jfqkmi xmicje xfiuwcfj* Hifxuqe fb wne xmh xnfuig ae gfje tcwncj 7> nfuqx .hmj
geims cb cw cx fjis cj wne x`cj#*
-
8/9/2019 Congenital Neurologic Disorders
70/114
\qfrcge kewchuifux x`cj nsdceje wf |qerejwcqqcwmwcfj* \qfrcge xweqcie gfudnjuw qcjd wf hfreq
wne iexcfj* Tmwhn bfq xcdjx fb cjhqemxe CH\*
Gf |mxxcre QFK e~eqhcxe wf ck|mcqeg ifteqe~wqekcwcex*
Xhqu|uifux |eqcjemi hmqe jehexxmqs*
-
8/9/2019 Congenital Neurologic Disorders
71/114
\fxw+F| Hmqe?
`ee| cj |qfje |fxcwcfj
kfjcwfq uqcje fuw|uw .bfq aimggeq cjouqs# kemxuqe nemg hcqhukbeqejhe gmcis
kfjcwfq kfrekejw fb ifteq e~wqekcwcex
-
8/9/2019 Congenital Neurologic Disorders
72/114
X|ehcbchJuqxcjd Cjweqrejwcfjxwfkseifkcjcjdfheie hicejwx
Ifjd weqk |qfaiekx fb cjbehwcfj mqe qeimweg wfuqcjmqs qewejwcfj) qebiu~ mjg hnqfjch UWC
m* wemhn hqege kmjeureq wf |mqejwx
a* Cjweqkcwwejw xeib hmwneweqczmwcfj hmj ae|eqbfqkeg mx emqis mx 5 2 semqx fb mde
h* Nsgqmwcfj mjg emqis qehfdjcwcfj fb UWCx
-
8/9/2019 Congenital Neurologic Disorders
73/114
Ejhe|nmifheie
@jftj aswne Imwcj jmke hqmjcukacbcguk) cx m jeuqmi wuae
gebehw hnmqmhweqczeg as xmh+ic`e |qfwquxcfjx fbwne aqmcj mjgwne kekaqmjex wnmw hfreq cwwnqfudn f|ejcjdx cj wne x`uii*Wnexe gebehwx mqe hmuxeg as
bmciuqe fb wne jeuqmi wuae wfhifxe hfk|ieweis guqcjd bewmigereif|kejw*
Ejhe|nmifheie
-
8/9/2019 Congenital Neurologic Disorders
74/114
Cjbmjw
-
8/9/2019 Congenital Neurologic Disorders
75/114
Ejhe|nmifheiex hmuxe m dqffre gftj wne kcggie fb
wne x`uii) fq aewteej wne bfqenemg mjg jfxe) fq fj
wne amh` xcge fb wne x`uii* Wne xereqcws fbejhe|nmifheie rmqcex) ge|ejgcjd fj cwx ifhmwcfj*
-
8/9/2019 Congenital Neurologic Disorders
76/114
Xcdjx mjg xsk|wfkx Ejhe|nmifheiex mqe fbwej mhhfk|mjceg as hqmjcfbmhcmi
majfqkmicwcex fq fwneq aqmcj kmibfqkmwcfjx*
Xsk|wfkx kms cjhiuge jeuqfifdch|qfaiekx) nsgqfhe|nmiux .heqeaqfx|cjmi biucgmhhukuimweg cj wne aqmcj#) x|mxwch}umgqc|iedcm .|mqmisxcx fb wne ickax#) kchqfhe|nmis .mjmajfqkmiis xkmii nemg#) mwm~cm .ujhffqgcjmweg kuxhie
kfrekejw#) gereif|kejwmi geims) rcxcfj |qfaiekx)kejwmi mjg dqftwn qewmqgmwcfj) mjg xeczuqex*
-
8/9/2019 Congenital Neurologic Disorders
77/114
Gcmdjfxcx
Uxumiis ejhe|nmifheiex mqe jfwchemaie gebfqkcwcex
mjg mqe gcmdjfxeg ckkegcmweis mbweq acqwn) auw m
xkmii ejhe|nmifheie cj wne jmxmi fq bfqenemg qedcfjhmj df ujgewehweg* Rmqcfux |nsxchmi mjg kejwmi
gereif|kejwmi geimsx hmj cjgchmwe wne |qexejhe fb
ejhe|nmifheiex*
-
8/9/2019 Congenital Neurologic Disorders
78/114
Wqemwkejw
Huqqejwis) wne fjis ebbehwcre wqemwkejw bfq
ejhe|nmifheiex cx qe|mqmwcre xuqdeqs) dejeqmiis
|eqbfqkeg guqcjd cjbmjhs* Wne e~wejw wf tnchn cw hmjae hfqqehweg ge|ejgx fj wne ifhmwcfj mjg xcze fb
wne ejhe|nmifheiex0 nftereq imqde |qfwquxcfjx hmj
ae qekfreg tcwnfuw hmuxcjd kmofq gcxmacicws*
-
8/9/2019 Congenital Neurologic Disorders
79/114
Xuqdeqs qe|fxcwcfjx wne auidcjd mqem amh` cjwf wne
x`uii) qekfrex wne |qfwquxcfjx) mjg hfqqehwx wne
gebfqkcwcex) ws|chmiis qeicercjd |qexxuqe wnmw hmjgeims jfqkmi aqmcj gereif|kejw*
Fhhmxcfjmiis) xnujwx mqe |imheg wf gqmcj e~hexx
heqeaqfx|cjmi biucg bqfk wne aqmcj*
-
8/9/2019 Congenital Neurologic Disorders
80/114
Wne dfmix fb wqemwkejw cjhiuge? hifxuqe fb f|ej x`cj gebehwx wf |qerejw cjbehwcfj
mjg gexchhmwcfj fb aqmcj wcxxue
qekfrmi fb jfjbujhwcfjmi e~wqmhqmjcmi heqeaqmi wcxxue tcwn tmweq+wcdnw hifxuqe fb wne guqm
wfwmi hqmjcfbmhcmi qehfjxwquhwcfj tcwn |mqwchuimq ek|nmxcx fjmrfcgcjd wne ifjd+jfxe gebfqkcws .jmxmi eifjdmwcfj wnmw qexuiwxbqfk ge|qexxcfj fb wne hqcacbfqk |imwe mjg jmxmi |imhfge#*Tcwnfuw |qf|eq kmjmdekejw) wne ifjd+jfxe gebfqkcws hmj aekfqe farcfux mbweq qe|mcq*
-
8/9/2019 Congenital Neurologic Disorders
81/114
\qckmqs Juqxcjd Cjweqrejwcfjx
\qerejw Cjbehwcfj
Hfreq wne xmh tcwn mj F*X* xfm`eg cj JXX
\qerejw hfjxwmjw wfuhncjd mjg nmjgicjd fb wne xmh
Gf jfw |qch` wne xmh
\imhe wne amas cj |fxcwcfjx wnmw |qerejwx wne
hfk|qexxcfj fb wne xmh
-
8/9/2019 Congenital Neurologic Disorders
82/114
Juqxcjd \qfaiekx bfq X|cjm Acbcgm mjg
Ejhe|nmifheie \fwejwcmi bfq cjbehwcfj
+ \qef|eqmwcreis) wne kmcj dfmi cx wf |qerejw qu|wuqe
fb xmh wf |qerejw cjbehwcfj m* \fxcwcfj cj |qfje fq cj mjs |fxcwcfj wnmw |qerejwx
hfk|qexxcfj fb wne xmh
a* Hfreq xmh tcwn kfcxwejeg dmuze
h* Hneh` xmh bfq wemqx fq hqmh`x
g* gf jfw hfreq xmh tcwn hifwncjd fb gcm|eq
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8/9/2019 Congenital Neurologic Disorders
83/114
e* \eqcjemi hmqe wf |qerejw hfjwmkcjmwcfj fb xmh b* Kfjcwfq bfq kmjcbexwmwcfj fb kejcjdcwcx
\fxwf|eqmwcreis \qfkfwe nemicjd mjg qeguhe jeuqfifdchmihfk|ichmwcfjx m* =* \fxcwcfj |qfje t& nemg xicdnwis ifteq wnmj wne afgs .X|cjm
Acbcgm#
m* 1* \fxcwcfj cj mjs |fxcwcfj wnmw |qerejwx ujgue hf|qexxcfj fb wnexuqdchmi xcwe tcwn nemg xicdnwis eiermweg .Ejhe|nmifheie#
a* |imhe |qfwehwcre amqqceq mhqfxx cjhcxcfj wf |qerejw hfjwmkcjmwcfj
-
8/9/2019 Congenital Neurologic Disorders
84/114
\fwejwcmi bfq cjouqs qeimweg wf Cjhqemxe CH\
Jeuqf hneh`x tcwn gmcis nemg hcqhukbeqejhe
Kfjcwfq xcdjx mjg xsk|wfkx fb cjhqemxe CH\
Cjxwquhw bmkcis qedmqgcjd qehfdjcwcfj fb xnujwcjbehwcfj& kmibujhwcfj
\imhe m xkmii |mg ujgeq wne ifteq |fqwcfj
fb wne iedx wf |qerejw fqwnf|egch |qfaiekx
-
8/9/2019 Congenital Neurologic Disorders
85/114
Cjebbehwcrebmkcis hf|cjd
\mqejwx tcii jeeg nei| gemicjd tcwn wne cxxue fb hnqfjch xfqqft mx teii mx wne ifjd weqk
mx|ehwx fb wne hfjgcwcfj Mjdeq mjg gejcmi
Mxxexx bmkcis xu||fqw mjg mrmcimaie qexfuqhex
Qekekaeq wnmw ereqs bmkcisx kewnfg fb hf|cjd
cx gcbbeqejw
-
8/9/2019 Congenital Neurologic Disorders
86/114
\qerejwcfjfbJeuqmi Wuaegebehwx
Tfkej tnf hfuig aehfke |qedjmjw mqe mgrcxeg wf
dew 7
-
8/9/2019 Congenital Neurologic Disorders
87/114
HFKKFJ NEMIWN
\QFAIEKX F
BWNE
HNCIG MJG
MGFIEXHEJW
-
8/9/2019 Congenital Neurologic Disorders
88/114
Heqeaqmi \mixsQesex Xsjgqfke
-
8/9/2019 Congenital Neurologic Disorders
89/114
HEQEAQMI \MIXS Kfwfq bujhwcfj ck|mcqkejw Gcbbchuiw cj hfjwqfiicjd wne rfiujwmqs kuxhiex gue
wf aqmcj cjouqs* Hmjjfw ae gcmdjfxeg emqis cj icbe jfw ujiexx wne
hncig xwmqweg wf kfre*
Kfxw hfkkfj |eqkmjejw gcxmacicws fb hncignffg* Ncdn qcx` amacex tcwn M\DMQ aeift 5
-
8/9/2019 Congenital Neurologic Disorders
90/114
-
8/9/2019 Congenital Neurologic Disorders
91/114
Xcdjx " Xsk|wfkx? .tcii rmqs mhh* wf |fqwcfjfb aqmcj wnmw cx gmkmde fq cjrfire#
+ Tem`jexx+ \mqmisxcx mjg cjhffqgcjmwcfj fb rfiujwmqskfrekejwx fb kuxhiex+ Xeczuqex
-
8/9/2019 Congenital Neurologic Disorders
92/114
+ rcxumi mjg nemqcjd gcbbchuiwcex+ ekfwcfjmi gcxfqgeqx .kffg xtcjdx)
cqqcwmacicws) majfqkmi |fxwuqe) xnfqwmwwejwcfj x|mj#) ck|uixcrejexx+ |qckcwcre qebie~ex+ x|eehn |qfaiek+ |ffq xtmiiftcjd
-
8/9/2019 Congenital Neurologic Disorders
93/114
-
8/9/2019 Congenital Neurologic Disorders
94/114
-
8/9/2019 Congenital Neurologic Disorders
95/114
Himxxcbchmwcfj?=* X|mxwch kuxhiex mqe ns|eqwfjch)
|eqxcxwejw jefjmwmi qebie~ex) |fxcwcreamacjx`c) hfjwqmhwuqex1* Bimhhcg kuxhiex tem`) xfbw) bimaas8* Mwnewfwch xjm`e fq tfqk+ic`e kfrekejw0
gcxm||emqx tnej mxiee| fq qeim~*
-
8/9/2019 Congenital Neurologic Disorders
96/114
-
8/9/2019 Congenital Neurologic Disorders
97/114
7* Qcdcg iemg+|c|e wfjchcws5* Mwm~ch |qckmqs cjhffqgcjmwcfj0 dmcw
mt`tmqg0 tcge+amxeg*2* Mwfjch imh` fb wfje fq jf qex|fjxe fb kuxhie
wf m xwckuic*
4* Wqekfq ujhfjwqfiimaie cjrfiujwmqs kfwcfjx fb
m qnswnkch miweqjmwcjd |ejguimq |mwweqj*
-
8/9/2019 Congenital Neurologic Disorders
98/114
Gcmdjfxcx?
Geimsegkfwfqgereif|kejw
\eqxcxwejw jefjmwmiqebie~ex
Xhcxxfqcjd
Wqemwkejw
Xsk|wfkmwch
Fqwnf|egch
\nsxchmi Wneqm|s
Qex|cqmwfqs
Wneqm|s
-
8/9/2019 Congenital Neurologic Disorders
99/114
Juqxcjd kmjmdekejw?
=* Mck? kuxhie qe+eguhmwcfj
|nsxcfwneqm|s |qfrcge jfj+xwckuimwcjd ejrcqfjkejw
-
8/9/2019 Congenital Neurologic Disorders
100/114
dcre kuxhie qeim~mjwx&mjwc+hfjruixmjwgqudx
kmcjwmcj xmbe ejrcqfjkejw .uxe xmbe wfsx# |qerejw bqfk mhhcgejwmi bmiix ejhfuqmde cjge|ejgejhe tncie
|qfrcgcjd mge}umwe juwqcwcfj . huw bffgcjwf xkmiieq |cehex#
-
8/9/2019 Congenital Neurologic Disorders
101/114
-
8/9/2019 Congenital Neurologic Disorders
102/114
-
8/9/2019 Congenital Neurologic Disorders
103/114
xeqre bffg wnmw xwch`x wf wne x|ffj ic`e kmxneg|fwmwf*
|fxcwcfj |mwcejw |qf|eqisgcxqedmqg kexxs emwcjd0 |uw aca*
miift hncig wf nfig wne x|ffj ducgcjd cw wf ncx kfuwn*
gcxhc|icje cx jehexxmqs bfq wne hncig wf beei wne ifre
mjg xehuqcws .gfjw freq|qfwehw#
-
8/9/2019 Congenital Neurologic Disorders
104/114
QESEX XSJGQFKE
Hnmqmhweqczeg as mhuwe ejhe|nmif|mwns mjgbmwws gedejeqmwcfj fb wne icreq mjg fwneq
magfkcjmi fqdmjx* Fhhuqx mbweq rcqmi ciijexx) |mqwchuimqis mbweq
UQC fq rmqcheiim .hnch`ej|f~# Mgkcjcxwqmwcfj fb mx|cqcj cx m hfjwcauwcjd
bmhwfq*
-
8/9/2019 Congenital Neurologic Disorders
105/114
Xcdjx " Xsk|wfkx?
+ UQC = 8 gmsx mbweq
+ Bereq+ Ne|mwch |qfaiek+ Gehqemxe ierei fb hfjxhcfuxjexx
+ Kmimcxe hfudn
-
8/9/2019 Congenital Neurologic Disorders
106/114
Gcmdjfxcx?
+ Icreq bujhwcfj wexw
+ MXW)XDFW) MIW) XD\W) IGN) xequkmkkfjcm iereix mqe eiermweg aehmuxefb |ffq icreq bujhwcfj*
+ Geimseg |qfwnqfkacj wcke
-
8/9/2019 Congenital Neurologic Disorders
107/114
Kmjmdekejw?+ Jeuqfifdch mxxexxkejw+ Kfjcwfq C&F .heqeaqmi egekm mjg
|qerejw gensgqmwcfj#+ Fxkfwch gcuqewchx .kmjjcwfi# kms aemgkcjcxweqeg wf qeguhe heqeaqmi
egekm
-
8/9/2019 Congenital Neurologic Disorders
108/114
+ Kfjcwfq diuhfxe ierei mjg aieegcjdwcke .ift aiffg diuhfxe ierei hmj
iemg wf xeczuqex0 |qfifjdeg aieegcjdwcke hmj cjgchmwe hfmduimwcfj|qfaiekx mx m qexuiw fb icreqgsxbujhwcfj*
+ Mrfcg uxe fb mx|cqcj
-
8/9/2019 Congenital Neurologic Disorders
109/114
QESEX XSJGQFKE
Hnmqmhweqczeg as mhuwe ejhe|nmif|mwns mjgbmwws gedejeqmwcfj fb wne icreq mjg fwneq
magfkcjmi fqdmjx* Fhhuqx mbweq rcqmi ciijexx) |mqwchuimqis mbweq
UQC fq rmqcheiim .hnch`ej|f~# Mgkcjcxwqmwcfj fb mx|cqcj cx m hfjwcauwcjd
bmhwfq*
-
8/9/2019 Congenital Neurologic Disorders
110/114
-
8/9/2019 Congenital Neurologic Disorders
111/114
Xcdjx " Xsk|wfkx?
+ UQC = 8 gmsx mbweq
+ Bereq+ Ne|mwch |qfaiek+ Gehqemxe ierei fb hfjxhcfuxjexx
+ Kmimcxe hfudn
-
8/9/2019 Congenital Neurologic Disorders
112/114
Gcmdjfxcx?+ Icreq bujhwcfj wexw
+ MXW)XDFW) MIW) XD\W) IGN
) xequkmkkfjcm iereix mqe eiermweg aehmuxefb |ffq icreq bujhwcfj*
+ Geimseg |qfwnqfkacj wcke
-
8/9/2019 Congenital Neurologic Disorders
113/114
Kmjmdekejw?+ Jeuqfifdch mxxexxkejw+ Kfjcwfq C&F .heqeaqmi egekm mjg
|qerejw gensgqmwcfj#+ Fxkfwch gcuqewchx .kmjjcwfi# kms ae
mgkcjcxweqeg wf qeguhe heqeaqmiegekm
-
8/9/2019 Congenital Neurologic Disorders
114/114
+ Kfjcwfq diuhfxe ierei mjg aieegcjdwcke .ift aiffg diuhfxe ierei hmj
iemg wf xeczuqex0 |qfifjdeg aieegcjdwcke hmj cjgchmwe hfmduimwcfj|qfaiekx mx m qexuiw fb icreqgsxbujhwcfj*
+ Mrfcg uxe fb mx|cqcj