RESEARCH Open Access ALS-linked misfolded SOD1 species have divergent impacts on mitochondria Sarah Pickles12 Sabrina Semmler14 Helen R Broom5 Laurie Destroismaisons1 Laurine…
EUKARYOTIC CELL Nov 2010 p 1669–1679 Vol 9 No 11 1535-977810$1200 doi:101128EC00191-10 Copyright © 2010 American Society for Microbiology All Rights Reserved Extracellular…
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Superoxide dismutase 1 encoding mutations linked to ALS adopts a spectrum of misfolded statesSuperoxide dismutase 1 encoding mutations linked to ALS adopts a spectrum of
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1 The E3 ubiquitin ligase TRAF6 is a novel interacting protein of amyotrophic lateral sclerosis-linked misfolded SOD1 Sabrina Semmler1,4, Myriam Gagné4,5, Pranav Garg7,…
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OPEN REVIEW Degradation of misfolded proteins in neurodegenerative diseases: therapeutic targets and strategies Aaron Ciechanover12 and Yong Tae Kwon1 Mammalian cells remove…
1 Arresting Amyloid with Coulomb’s Law: Acetylation of ALS-Linked SOD1 by Aspirin Impedes Aggregation. Alireza Abdolvahabi a , Yunhua Shi a , Nicholas R. Rhodes a , Nathan…
'lb JOURNAL OF BIOUCICAL C m s ~ n v 0 1994 by The American Society for Biochemistry and Molecular Biology, Inc Vol. 269, No. 9, Issue of March 4, pp. 6874-6877, 1994 Printed…
Misfolded SOD1 pathology in sporadic Amyotrophic Lateral Sclerosiswww.nature.com/scientificreports Misfolded SOD1 pathology in sporadic Amyotrophic Lateral Sclerosis Bastien
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γD-crystallin aggregation precursor 1 An internal disulfide locks a misfolded aggregation-prone intermediate in cataract-linked mutants of human γD-crystallin Eugene Serebryany*1,…
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