Short QT Syndrome:Diagnostic Alogarithm
-
Upload
nizams-institute-of-medical-sciences -
Category
Health & Medicine
-
view
681 -
download
0
description
Transcript of Short QT Syndrome:Diagnostic Alogarithm
![Page 1: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/1.jpg)
Short QT syndromeA diagnostic scoring system
![Page 2: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/2.jpg)
Algorithm
Personal HistoryFamily HistoryTake a 12 lead ECGLook at genetic report
![Page 3: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/3.jpg)
Personal History
FEATURES SCORES
History of sudden cardiac arrest 2
Documented PMVT or VF 2
Unexplained syncope 1
Atrial fibrillation 1
![Page 4: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/4.jpg)
Family History
FEATURES SCORE
First- or second-degree relative with high probability of SQT
2
First- or second-degree relative with autopsy-negative SCD
1
Sudden infant death syndrome 1
![Page 5: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/5.jpg)
12 lead ECG
Corrected QT interval in ms score
<370 1
<350 2
<330 3
J point peak to T-wave interval<120 msec
1
![Page 6: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/6.jpg)
GENETIC STUDY
GENOTYPE SCORE
Geno type positive 2
Mutation of undetermined significance in a culprit gene
1
![Page 7: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/7.jpg)
Interpretation
A score > 4 indicates high ProbabilityA score > 3 indicates intermediate
probabilityA score > 2 indicates low probability
This scoring system requires at least 1 point from ECG section before evaluating other data
![Page 8: Short QT Syndrome:Diagnostic Alogarithm](https://reader036.fdocuments.net/reader036/viewer/2022082623/545c5806b0af9fa92c8b4732/html5/thumbnails/8.jpg)
THANK YOU