Registro Nacional de Hemopatías Malignas Presidente: Dra. Adriana Cardeza Monitora de datos: Dra....
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Transcript of Registro Nacional de Hemopatías Malignas Presidente: Dra. Adriana Cardeza Monitora de datos: Dra....
![Page 1: Registro Nacional de Hemopatías Malignas Presidente: Dra. Adriana Cardeza Monitora de datos: Dra. Carolina Oliver.](https://reader035.fdocuments.net/reader035/viewer/2022062808/5665b42c1a28abb57c8fc4ed/html5/thumbnails/1.jpg)
Registro Nacional de Hemopatías Malignas
Presidente: Dra. Adriana CardezaMonitora de datos: Dra. Carolina Oliver
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IC-APL
2007-2014
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32 IC-APL pts.
APL 2007-2014: total 59 pts. 27 pts. other protocols
ACUTE LEUKEMIA REGISTRY
AML incidence rate: 3/100.000/year
APL incidence rate: 0.09- 0.3 /100.000/year.
APL: 8-9 % of AML
URUGUAY IC-APL DATA 2007-2014___________________________________
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URUGUAY IC-APL PATIENTS 2007-2014
• Median age: 34 years (15-76)• Median Follow up: 27 month (3-86)
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URUGUAY IC-APL PATIENTS 2007-2014
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IC-APL Trial: Induction response
Patients under induction therapy 0/32
Patients achieving CR after induction phase 28/32 (4 death at ind)
Patients under consolidation 3/28
Patients who have completed consolidation 24/28 (1 death at 2nd)
Patients PML-RAR negative at the end of consolidation 23/24(1 positive and died)
Patients under maintenance therapy 8/22(1 died because of LAM M5
during maintainance)
Relapse (after 3th consolidation). 1/22(died in relapse after 3th
consolidation)
Patients off therapy 14/22
IC-APL Trial: Consolidation therapy and beyond
_______________________________________________
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CAUSES OF DEATH
• CNS bleeding: during induction. – 2 high risk– 1 intermediate
• Infections: – 1 patient after 1°
consolidation– 1 during induction– 1 in clinical relapse.
• 2° Neoplasm: AML M5b MLL and t(9;11) at 11 month after M3 was diagnosticed.
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LEUCEMIAS AGUDAS
7º año de registro
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LA DEBUT 2007-2014
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LA INCIDENCIA 2007-2014
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LA 7º AÑO DE REGISTRO1-09-2013 – 31-08-2014
LAM LAL
F: 31 F: 21
M: 48 M: 30
79 51
TOTAL: 130 casos nuevos
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LA SEGÚN EDAD2007-2014
AÑO NUMERO DE CASOS
MEDIANA EDAD MINIMO MAXIMO
2007-2008 137 49 1 882008-2009 146 51 2 882009-2010 134 65 0 952010-2011 168 57 0 902011-2012 125 47 0 992012-2013 136 53 0 932013-2014 130 46 0 92
MEDIANA DE EDAD 2011-2012
NIÑOS ADULTOS
LAM RANGO LAL RANGO LAM RANGO LAL RANGO
2,5 1-13 8 0-15 años 62 17-92 33 15-75
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LLC
6º año de registro
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RESUMEN DE REGISTRO1-09-08 – 31-08-2014
AÑO NUEVOS CASOS
MEDIANA DE EDAD
RELACION M/F CD 38 +(% DE LOS QUE
HAY DATOS APORTADOS)
2008-2009 172 72 2:1
2009-2010 142 71 1,5:1
2010-2011 186 72 2:1 23
2011-2012 171 73 1,5:1 14
2012-2013 192 71 2:1 25
2013-2014 221 71 2:1 23
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LLC1-09-13 – 31-08-14
221 nuevos casos Mediana edad: 71 años
Rango 26-94 años
Tasa de Incidencia:7,29/100.000 hab/año
CD 38 +: 23 %
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Nº DE NUEVOS CASOS POR AÑO
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LLC INCIDENCIAx 100.000 HABITANTES/AÑO
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COLABORAN: