HEME SYNTHESIS
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Succinyl CoA Glycine δ- Aminolevulinate 2 δ- Aminolevulinate Porphobilinogen 4-Porphobilinogen Uroporphyrinogen III Coproporphyrinogen III Protoporphyrinogen III Protoporphyrin IX Heme δ- Aminolevulinate Synthase δ- Aminolevulinate dehydratase Uroporphyrinogen I Synthase & uroporphyrinogen III cosynthase Uroporphyrinogen decarboxylase Coprophyrinogen oxidase Protophyrinogen oxidase Ferrochelatase Fe 2+ 4H + 4CO 2 4CO 2 4NH 3 4H 2 O CoASH Synthesis of heme
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Transcript of HEME SYNTHESIS
Succinyl CoA Glycine
δ- Aminolevulinate
2 δ- Aminolevulinate
Porphobilinogen
4-Porphobilinogen
Uroporphyrinogen III
Coproporphyrinogen III
Protoporphyrinogen III
Protoporphyrin IX
Heme
δ- AminolevulinateSynthase
δ- Aminolevulinatedehydratase
Uroporphyrinogen I Synthase &
uroporphyrinogenIII cosynthase
Uroporphyrinogendecarboxylase
Coprophyrinogenoxidase
Protophyrinogenoxidase
FerrochelataseFe2+
4H+
4CO2
4CO2
4NH3
4H2O
CoASH
Synthesis of heme