Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach...

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Duke Cameron, MD Division of Cardiac Surgery Division of Cardiac Surgery

Transcript of Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach...

Page 1: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Duke Cameron, MDDivision of Cardiac SurgeryDivision of Cardiac Surgery

Page 2: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

No financial disclosures

No disclosures

No financial disclosures

Acknowledgement of Drs.Vricella, Black and Dietz

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Page 3: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Loeys-Dietz Syndrome

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Page 4: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

LDS Aortopathy

• Root Aneurysm• Root Aneurysm

• Arterial Tortuosity

• Dissection/Rupture at• Dissection/Rupture atyoung age and smallaortic sizeaortic size

• Peripheral aneurysms• Peripheral aneurysms

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Page 5: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Aortic Root Replacement in LDS

5 79 LDS operations

Page 6: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Operative Experience with LDS

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Page 7: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

ARR in LDS: Operative Technique

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Bentall Reimplantation VSRR

Page 8: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

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Page 9: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Concomitant Procedures

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Page 10: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Operative Results

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Page 11: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

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Page 12: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Late Results

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No reoperations for AR in trileaflet David VSRRs

Page 13: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Special Considerations

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Page 14: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Coronary artery button aneurysms

“Hershey Kiss” aneurysms

Page 15: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Arch Reinterventions in LDS

Mos

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Page 16: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

LVOT Pseudoaneurysm

• Typically arising from subanular• Typically arising from subanularsutures in NC sinus, thru aorto-mitral apron

• Can be PSA or fistula to LA or• Can be PSA or fistula to LA orRA

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Page 17: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Conclusions: ARR in LDS

• Low operative risk (0% mortality)

• Valve sparing operations have good• Valve sparing operations have goodearly and midterm results

• High re-intervention rate• High re-intervention rate

• Close surveillance necessary postop• Close surveillance necessary postop

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Page 18: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding

Recommendations

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Page 19: Duke Cameron, MD Division of Cardiac SurgeryCerebrovascular Arteries Individualized approach Descending Thoracic Aorta Abdominal Aorta Visceral/lliac Arteries 4.5-5 cm or rapidly expanding