Brain & Development Volume 8, 1986

Issue Text Pages

1 (February) 1 - 84

2 (April) 85 - 232

3 (June) 233 - 322

4 (August) 323 - 494

5 (October) 495 - 574

6 (December) 575 - 666

Contents of Volume 8 Invited Review Article Cerebral Dysgeneses and Their Influence on Fetal Muscle Development

Sarnat HE - ...... .. . . ..... ...... .. ...... ........ .... ...... .. ........ .. .. .... .... ........ .... .. ...... .... .. .. .. ..

Special Reading Learning of Disabled Children and Their Environment

495

Hanada M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. . . . . . . . . . 547

Original Articles Brain Maturity in Regard to the Auditory Brainstem Response in Small-for-Date Neonates

Saintonge J, Lavoie A , Lachapelle J, COte R .. .... . .. ... ... . ... . .. . ... . .. . . .

Developmental Change of Short Latency Somatosensory Evoked Potential Waves between P3 and Nt Components in Children

Nishimura S, Tomita Y, Tanaka T, Kasagi S: Takashima S, Takeshita K . . . . . . . . . . . . . . . 6

Somatosensory Evoked Potentials to Posterior Tibial Nerve Stimulation in Children Zhu Y, Georgesco M, Cadi/hac J . . . . .. . . . ... .... .. . . . . .. . . . .. ... . .. . . .. 10

Superoxide Dismutase in Fetal Rat Cerebrum X-Irradiated in Utero Suzuki H, Tanaka H, Iwasaki S, A rima M .. . ......... . ....... . .. .. . . ...... 17

Pathogenesis of Periventricular White Matter Hemorrhages in Pre term Infants Takashima S, Mito T, Ando Y . . .............................. . .... . ... 25

Cranial Ultrasound in the Detection of Post meningitic Complications in the Neonates Hung KL ..................... . ......... . ... . .... .. ... .. .... . ... 3 1

Pedoscope Studies on Neonatal Activity and Center of Gravity after Delivery Maeka wa K, Soeda A, Yokoi S, Maekawa N, Usu i N, Kiryu T, Hirasawa Y, Akamatsu H, Kamanaka A, Wada M, Yanagihara K .. . .... .. ... . .............. 37

Sodium Valproate Monotherapy in Childhood Epilepsy Dulac 0, Steru D, Rey E, Perret A, Arthuis M . .. ... . ......... .. .. .. .. ... . . . 47

Pharmacokinetics of Rectal Diazepam in the Prevention of Recurrent Febrile Convulsions

Minagawa K, Miura H, Mizuno S, Shirai H . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 53

Syndrome of Septo-optic-Pituitary Dysplasia: The Clinical Spectrum Morishima A, Aranoff GS ............... . . . ... .. .. .. ... . ........... , 233

The Effect of Neonatal Hyperbilirubinemia on the Auditory Brainstem Response Kuriyama M, Konishi Y, Mikawa H . .. ... . ...... . .... . . .. . . .. .. . .. .. ... 240

648 Brain & Development, Vol 8, No 6, 1986

Auditory Brain Stem Responses (ABR) in Developmentally Retarded Infants and Children

Mochizuki Y, Ohkubo H, Yoshida A, Tatara T . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 246

Serum and Urinary Carnitine and Organic Acids in Reye Syndrome and Reye-like Syndrome

Sugimoto T, Nishida N, Woo M, Takeuchi T, Yasuhara A, Kobayashi Y, Sakane Y 257

Ultrasound Measurement of the Ventricular Size in Newborn Infants Liao MF, Chaou WT, Tsao LY, Nishida H, Sakanoue M . . . . . . . . . . . . . . . . . . . . . .. 262

Quantitative Synaptic Changes on Purkinje Cell Dendritic Spines of Rats Born from Streptozotocin-induced Diabetic Mothers

Yamano T, Shimada M, Fujizeki Y, Kawasaki H, Onaga A ..................... 269

Hypoxic-Ischemic Brain Damage and Cerebral Blood Flow Changes in Young Rabbits Takashima S, Ando Y, Takeshita K .................................... 274

Suppression of 2',3'-Cyclic Nucleotide 3'-Phosphohydrolase Activity in Suckling Rat Brain by ACTH

Izumi T, Shishikura K, Fukuyama Y ................................... 500

Ultrasonographic Evaluation of Cavum Septi Pellucidi and Cavum Vergae Nakajima Y, Yano S, Kuramatsu T, Ichihashi K, Miyao M, Yanagisawa M, Itoh K ....................................................... 505

High Incidence of Fundus Hamartomas and Clinical Significance of a Fundus Score in Tuberous Sclerosis

Kiribuchi K, Uchida Y, Fukuyama Y, Maruyama H . . . . . . . . . . . . . . . . . . . . . . . . .. 509

A Golgi Study of the Polymicrogyric Cortex in Aicardi Syndrome Ferrel I, Cusi MV, Liarte A, Campistol J . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 518

Muscle Fiber Type Transformation in Nemaline Myopathy and Congenital Fiber Type Disproportion

Miike T, Ohtani Y, Tamari H, Ishitsu T, Une Y. . . . . . . . . . . . . . . . . . . . . . . . . . . .. 526

Administration of ACTH to Suckling Rats Results in Hyperkinetic Behavior Izumi T, Fukuyama Y, Nomoto T, Kato N ............................... 575

The Developmental Changes of the Extracerebral Space Seen Ultrasonography in Neonates and Infants

Ando Y, Kawahara H, Takashima S, Kadono T, Maeda K, Takeshita K, Ohta S . . . . . . .. 580

Sleep Study on Patients with Severe Brain Damage-Polysomnographical Examination -

Kohyama J, Shishikura J, Nakano I, Iwakawa Y, Mori K ...................... 583

Neurophysiological Studies in the Leigh Syndrome Van Erven PMM, Colon EJ, Gabreels FJM, Renier WO, Vingerhoets DM . . . . . . . . . . .. 590

Cerebral Blood Flow and Brain Shrinkage Seen on CT during ACTH Therapy Futagi Y, Abe J, Kawahihashi K ...................................... 596

Case Reports Encephalopathy in Compensated Hashimoto Thyroiditis: A Clinical Expression of Autoimmune Cerebral Vasculitis

Shein M, Apter A, Dickerman Z, Tyano S, Gadoth N . . . . . . . . . . . . . . . . . . . . . . . . .. 60

Unusual Case of Diffuse Connective Tissue Disease with Nodule Formations in Muscle, Lung, Kidney and Brain

Nobukuni Y, Miike T, Ohtani Y, Tsuchiya H, Nunoi H, Hattori S, Matsuda I . . . . . . . . .. 64

Stroke in a Patient with Hemolytic-Uremic Syndrome with a Good Outcome Steinberg A, Ish-Morowitcz M, EI-Peleg 0, Mor J, Branski D . . . . . . . . . . . . . . . . . . . .. 70

Valproic Acid in Neonatal Status Convulsivus Steinberg A, Shalev RS, Amir N ...................................... 278

Contents of Volume 8 649

Ten Years Follow Up Study of Steroid Therapy for Congenital Encephalomyopathy

Kinoshita M, Nishina M, Koya N . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 280

Progressive Muscular Dystrophy with Congenital Adrenal Hypoplasia: An Unusual Autopsy Case

Toyofuku T, Takashima S, Takeshita K, Nagafuji H ......................... 285

Mitochondrial Cytopathy with Lactic Acidosis, Carnitine Deficiency and De Toni-Fanconi-Debre Syndrome

Kitano A, Nishiyama S, Miike T, Hattori S, Ohtani Y, Matsuda I .................. 289

A Case of Hereditary Motor and Sensory Neuropathy Type III with a Decrease in Unmyelinated Fibers

Narazaki 0, Hanai T, Sakamoto K, Ohnishi A ............................. 295

An Autosomal Dominant Type of Congenital Muscular Dystrophy Ley ten QH, Gabreels, Joosten EMG, Renier WO, Ter Laak HJ Ter Haar BGA, Stadhouders AM . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 533

A Case of Brainstem Encephalitis with CT Scan Abnormality Mimicking Fisher Syndrome

Tachi N, Tsuzuki Y, Minami R ....................................... 538

Cornelia de Lange Syndrome Associated with a Suprasellar Germinoma Sugita K, Izumi T, Yamaguchi K, Fukuyama Y, Sato A, Kajita A . . . . . . . . . . . . . . . .. 541

Acute Encephalopathy with Hyperammonemia and Dicarboxylic Aciduria during Calcium Hopantenate Therapy: A Patient Report

Kimura A, Yoshida I, Ono E, Matsuishi T, Yoshino M, Yamashita F, Yamamoto M, Hashimoto T, Shinka T, Kuhara T, Matsumoto I . . . . . . . . . . . . . . . . .. 601

Neuroaxonal Dystrophy of Neonatal Onset with Unusual Clinicopathological Findings

Tachibana H, Hayashi T, Kajii T, Takashima S, Sasaki K ...................... 605

A Case Report of Infantile Striatal Necrosis with an Acute Onset Yasukohchi S, Akabane T, Mori T, Tamagawa K, Morimatsu Y . . . . . . . . . . . . . . . . .. 609

Congenital Muscular Dystrophy with Cerebral and Ocular Malformations (Cerebro-Oculo-Muscular Syndrome)

Heyer R, Ehrich J, Goebel H-H, Christen H-J, Hanefeld F . . . . . . . . . . . . . . . . . . . . .. 614

Clinical Features in a Girl with Duchenne Muscular Dystrophy with an X-Autosome Translocation; (X;4)(p2l ;q26)

Kimura S, Mitsuda T, Misugi N, Saito F, Tonomura A, Sugita H ................. 619

Muscular Alteration in Agyria with Pyramidal Tract Anomaly Hori A, Bardosi A, Goebel HH, Roessmann U ............................. 624

A Case of Ataxic Diplegia, Mental Retardation, Congenital Nystagmus and Abnormal Auditory Brain Stem Responses Showing Only Waves I and II

Aiba K, Yokochi K, Ishikawa T . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 630

The Syndrome of the Absence of a Septum Pellucid urn with Porencephaly Shimozawa N, Ohno K, Takashima S, Takakura H, Sugitani A . . . . . . . . . . . . . . . . . .. 632

A Clinical Trial of Interferon Therapy in a Case of Rapidly Progressive SSPE Sone S, Maeda K, Haginoya K, Sakuragawa N, Kisa T, Yoshioka H, Arima M . . . . . . . .. 636

Short Communications Increased Cadmium Resistance of Skin Fibroblasts from Menkes Disease Patients

Hayashi A, Sato M, Arima M, Aoki T . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 73

The Protective Effects of Vitamin E against Microcephaly in Rats X-Irradiated in Utero: Dendritic Branches

Tanaka H, Inomata K, Nishimura S, Arima M . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 301

650 Brain & Development, Vol 8, No 6,1986

The Value of Immediate Post-Operative Routine CT Related to Uncomplicated Ventricle Drainage in Childhood Hydrocephalus

Vles JSH, Casaer P, Lodder J, Plets C . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 552

Brazilian Girl with the Rett Syndrome Rosemberg S, Arita FN, Campos C . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 554

Letters to the Editor High-Dose Intravenous Methyl-Prednisolone in Chronic Polymyositis/ Dermatomyositis

Castro-Gago M, Alvez-Gonzalez F, PeNa-GuitiAn J . . . . . . . . . . . . . . . . . . . . . . . . .. 570

A Case of Heredo-Ataxia in a Subject with Karyotype 49 XXXXY Stanzani P, Bruno L, Pollari Maglietta E, Sorrenti G, Gobbi G . . . . . . . . . . . . . . . . . .. 570

Around the World The Child Neurology Society of China: The Past and the Present

Zuo C-H ...................................................... 567

The Proceedings of the 27th Annual Meeting of the Japanese Society of Child Neurology. Tokyo. July 18-20. 1985 Contents. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 85

Preface KimuraM ...................................................... 99

Special Lectures Syndrome of Septo-Optic-Pituitary Dysplasia

Morishima A, A ran off G ......................................... 100 Iron Metabolism in Brain

Swaiman KF . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 101 The Effects of Antiepileptic Drugs on Developing Neurons in Culture

Sher PK, Neale EA, Graubard BI, Habig W, Fitzgerald SC, Nelson PG . . . . . . . . . . .. 102

Forum Pediatric Neurology Training in America

Swaiman KF . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 103 Symposium

Neurological Disordres in Children and Immunization . . . . . . . . . . . . . . . . . . . . . . .. 104 Free Papers

Experimental Developmental Neurobiology Abstr no 1-12 .................... 108 Human Development Abstr no 13-21 .................................. 114 Neurophysiological Diagnostic Procedures Abstr no 22-38 .................... 118 Neuroradio10gical and Neurochemical Diagnostics Abstr no 39-45 ............... 127 Congenital Anomalies of the Nervous System Abstr no 46-60 .................. 130 Neonatal Neurology Abstr no 61-71 ................................... 138 Neurocutaneous Syndromes Abstr no 72-77 . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 143 Intellectual, Motor and Sensory Disturbances Abstr no 78-83 .................. 146 Convulsive Disordres Abstr no 84-115 . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 149 Anticonvu1sants - Pharmacology and Side Effects Abstr no 116-131 . . . . . . . . . . . . .. 165 CNS Infections-Neuroimmuno10gy Abstr no 132-150. . . . . . . . . . . . . . . . . . . . . .. 173 Vascular and Surgical Disorders Abstr no 151-159 . . . . . . . . . . . . . . . . . . . . . . . . .. 183 Heredodegenerative or Etiology Unknown Abstr no 160-174 . . . . . . . . . . . . . . . . . .. 187 Neuropsychiatric and Systemic Disorders Abstr no 175-183 ................... 195 Neurometabolic Disorders Abstr no 184-203 ............................. 199 Spinal Cord, Peripheral Nerves and N-M Junction Abstr no 204-214 . . . . . . . . . . . . .. 210 Muscle Disorders Abstr no 215-241 ................................... 215 Miscellaneous Abstr no 242-244 . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 229

Contents of Volume 8 651

The Symposium on Developmental Neurobiology, Tokyo, November 3-4, 1984 Contents. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 325

Preface and Introductory Remarks Segawa M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 327

Brainstem, Midbrain and Behavior A. Serotonergic Neuron and Behavior

Development of 5HT Neuron Fujimiya M, Hosoda S, Kitahama K, Kimura H, Maeda T . . . . . . . . . . . . . . . . . . .. 335

Midbrain Raphe Neurons Imai H, Park MR, Steindler DA, Kitai ST. . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 343

5HT Neurons in Human Fetal CNS Takahashi H, Nakashima S, Ohama E, Takeda S, Ikuta F . . . . . . . . . . . . . . . . . . .. 355

Restricted Access to Natural Mother Shimoda K, Hanada K, Yamada N, Takahashi K . . . . . . . . . . . . . . . . . . . . . . . . .. 366

Rhythm of Midbrain-Lesioned Rats Takahashi K, Shimoda K, Yamada N, Sasaki Y, Hayashi S ................... 373

B. Dopaminergic Neuron and Behavior Monoaminergic System and REM Sleep

Mirmiran M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 382 Methamphetamine-Treated Pups

Sato M, Fujiwara Y . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 390 Circadian Rhythm in Infant Rats

Honma K, Honma S ............................................ 397

C. Midbrain, Brainstem Structures and Stage Setting Central Mechanisms of Paradoxical Sleep

Sakai K ..................................................... 402 Excitability Level-Setting Mechanisms in the Pons

Mori S, Ohta Y, Sakamoto T, Nonaka S ............................... 408

D. Clinical Symptoms in Relation to Midbrain and Brainstem Structures Effect of Alpha-Methyldopa

Shimohira M, Kohyama J, Kawano Y, Suzuki H, Ogiso M, Iwakawa Y ........... 416 Plasma Free Tryptophan in Autism

Hoshino Y, Yamamoto T, Kaneko M, Kumashiro H ....................... 424 SSEP in Autism

Hashimoto T, Tayama M, Miyao M .................................. 428 Polygraphical Study on Epilepsy

Iwakawa Y, Ogiso M, Suzuki H, Kawano Y, Koyama J, Shimohira M ...... . . . . .. 433 Brainstem Lesions in Infantile Spasms

Satoh J, Mizutani T, Morimatsu Y . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 443

Telencephalon and Behavior Dentate Responses in Amygdaloid Kindling

Uno M, Ozawa N .............................................. 451 Neural Activities in Monkey Basal Ganglia

Hikosaka 0, Sakamoto M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 454

Neurohormone, Neuropeptide and Behavior Prenatal Androgen and Preoptic Area

Ito S, Murakami S, Yamanouchi K, Ami Y ............................. 463 Sleep and Sleep Substances

Inoue S ..................................................... 469

Sleep Studies and Its Usefulness in the Analysis of Behavior Polysommongraphy

Segawa M, Nomura Y, Hakamada S, Nagata E, Sakamoto M, Oka N ............. 475

652 Brain & Development, Vol 8, No 6, 1986

Analysis of the Sleep-Wake Cycle Borbely AA . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 482

Closing Remarks Segawa M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 489

Invited Review Article Cerebral Dysgeneses and Their Influence on Fetal Muscle Development

Sarnat HB . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 495

Special Reading Learning of Disabled Children and Their Environment

Hanada M . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 547

Abstracts from 12th Annual Conference on Childhood Epilepsies in Kanto District, Tokyo, March 23, 1985 . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 305

Abstract from the Eighth Conference on Febrile Convulsions, Tokyo, December 14, 1985 .............................................. 557

Announcements of 5th ISDD . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 79 Announcement of the Neuromuscular Disease Symposium . . . . . . . . . . . . . . . . . . .. 572, 645 The Program of the 16th Meeting of the Chugoku-Shikoku Study Group on Infantile Spasms and Allied Disorders. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 315 The Programs of the 2nd and 3rd Meeting of the Pediatric Neuromuscular Disorder's CLub . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 643 The Program of the 1986 Annual Meeting of the Israel Society of Child Neurology. . . . . .. 644 15th Annual Meeting of Child Neurology Society . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 80 JSCN Call for Papers . ............................................ 572,642 Book Reviews ............................................ 77 78 315 641 Personnel ................................................. : .. ' 316: 645 Schedule of Meetings. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 80, 316,646 Contents of Volume 8 . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 648 Subject Index .................................................... 654 Author Index. . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . . .. 659

Contents of Volume 8 653