Chapter 53 Chapter 53 Osteogenesis Imperfecta and Other Defects of Bone Development as Occasional...
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Transcript of Chapter 53 Chapter 53 Osteogenesis Imperfecta and Other Defects of Bone Development as Occasional...
Chapter 53Chapter 53
Osteogenesis Imperfecta and Other Defects of Bone Development as
Occasional Causes of Adult Osteoporosis
Copyright © 2013 Elsevier Inc. All rights reserved.
Copyright © 2013 Elsevier Inc. All rights reserved.
FIGURE 53.1 Collagen biosynthesis.
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FIGURE 53.2 Osteogenesis imperfecta type I.
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FIGURE 53.3 Blue sclerae in osteogenesis imperfecta.
Copyright © 2013 Elsevier Inc. All rights reserved.
FIGURE 53.4 Triangular facies in osteogenesis imperfecta.
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FIGURE 53.5 Osteogenesis imperfecta type I.
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FIGURE 53.6 Osteogenesis imperfecta type II.
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FIGURE 53.7 A and B
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FIGURE 53.8 Osteogenesis imperfecta type III.
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FIGURE 53.9 Osteogenesis imperfecta type III.
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FIGURE 53.10 Osteogenesis imperfecta type IV.
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FIGURE 53.11 Osteogenesis imperfecta type V.
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FIGURE 53.12 Osteogenesis imperfecta type VII, (A) Patient age 3 years 5 months, showing selective shortening of the humeri (rhizomelia). (B) Patient V-6, age 4 months, showing bilateral coxa vara. Bowing deformity of the lower extremities is also evident. Source: Ward et al. (2002) [80].
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FIGURE 53.13 Osteogenesis imperfecta type VIII.