BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen...

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BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Transcript of BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen...

Page 2: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 3: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Paediatric ultrasound: Something slightlydifferent!

• First choice imaging modality in paediatric radiology• CT and MRI only in selected cases

• Different diseases, e.g.:• Intussusception

• Malrotation and volvulus

• Appendicitis

• Different proportions

• Smaller

• Less fat!

Page 4: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Paediatric ultrasound: Something slightlydifferent!

• First choice imaging modality in paediatric radiology• CT and MRI only in selected cases

• Different diseases, e.g.:• Intussusception

• Malrotation and volvulus

• Appendicitis

• Different proportions

• Smaller

• Less fat!

Page 5: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

The right approach

• Patience

• Involve the parents/guardians• Get them to help

• It might make or break the examiation

• Be gentle but diagnostic

• Use warm gel

• Keep thinking (goes for adult as well)

• Use high frequency probes (it’s amazing)

Page 6: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 7: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

What to consider…

Neonates

•Atresia (oesophagus,

stomach, bowel)

•Malrotation with volvulus

•Hirschsprung disease

•Meconium plug syndrome

•Meconium ileus

•Necrotising enterocolitis

(NEC)

Toddlers/Infants

•Gastroenteritis

•Intussusception

•Malrotation and volvulus

•Appendicitis

•Abdominal malignancy

•Meckels diverticulum

•Hemolytic uremic

syndrome

Children/Adolescents

•Appendicitis

•Inflammatory bowel disease

•IgA vasculitis

•Ovarium torsion

•Meckels diverticulum

•Abdominal malignancy

•Pancreatitis

•Distal intestinal obstruction

syndrome

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Case 1

• GA 37 weeks

• 2 days old

• Bilious vomiting since 1 day

• Abdominal distension

• No fever

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Differential diagnosis?

• Malrotation with volvulus

• Proximal bowel obstruction• Duodenal/jejunal atresia/stenosis

• Annular pancreas

• Distal bowel obstruction• Meconium ileus

• M. Hirshsprung

• Atresia

• Sepsis

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Volvulus or atresia?

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• a

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Different patient

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Normal

Applegate et al. Intestinal Malrotation in Children: A Problem-solvingApproach to the Upper Gastrointestinal Series

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• 720° volvulus

• Ladds procedure with derotation

• No bowel necrosis and good recovery

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Case 2

• GA 35 weeks

• 2 days old

• Weight 1300 grams

• Respiratory distress (saturation 85%)

• Abdominal distension

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Differential diagnosis?

• Necrotising enterocolitis (NEC)

• Sepsis

• Bowel obstruction

• Tumor

Page 19: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

• 24 uur postpartum

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Pneumatosis intestinalis

Met dank aan Simon Robben, MUMC Courtesy of prof. Simon Robben

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Over time…

• Progressive abdominal distension

• Blood in stool

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• 1 dag later

Page 23: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Necrotising enterocolitis (NEC)

http://www.chla.org/necrotizing-enterocolitis

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Case 3

• 1 year old boy

• Flown in from St. Maarten

• Cystic Nephroma seen on ultrasound

Courtesy of dr. Eric Beek

Page 26: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Differential diagnosis?

• Hydronephrosis

• Cyst originating from…• Kidney

• Spleen

• Pancreas

• Duplication

• Mesenteric cyst

• (multilocular) Cystic nephroma?

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High frequency probe! (12 MhZ)

Page 30: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Case 4

• 9 year old boy

• Blood in stool

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Between umbilicus and bladder

Courtesy of dr. Eric Beek

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Bowel wall layers

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Between umbilicus and bladder

Courtesy of dr. Eric Beek

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Differential diagnosis

• Duplication cyst

• (inflamed) Meckels diverticulum

Page 37: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Complications

• Hemorrhage

• Volvulus

• Intussusception

• Inflammation

• Confused with appendicitis

Ayati et al. Delayed Imaging for Detection of Meckel's Diverticulum in Tc99m Pertechnetate Scintigraphy

99m Tc pertechnetate scintigraphy

Page 38: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Case 5

• 4 year old

• Got hit by a car (5 miles/hour), hit on the leg

• 7 days ago

• Pain started 2 days after the accident

• Persisting severe abdominal pain

Page 39: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 40: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Page 42: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Normal appendix

Page 46: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Keep thinking

• Read the request form

• Talk to the clinician

• Ask critical questions

• Talk to the child• Where does it hurt?

• Keep an open mind

Page 47: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Case 6

• 3 year old girl

• Intermittent abdominal pain for 2 days

• No fever

• Bloody stool

Page 48: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Ultrasound!

Page 49: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Large bowel intussusception

• Diameter≥ 2.5 cm

• Intussusception includes mesenterial fat and lymph nodes

• Most commonly ileocolic

Page 50: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Small bowel intussusception

• Almost always an incidental finding• Asymptomatic

• Resolves during examination

• Associated with celiac disease and malabsorption syndromes

Page 51: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Treatment

• Repositioning• Spontaneous

• Pneumatic

• Hydrostatic

• Surgery

• Aim: overflow of air/fluid in small bowel• Ileocecal valve is usally edematous

• Complication: Perforation

Page 52: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Treatment

• Repositioning• Spontaneous

• Pneumatic• Hydrostatic

• Surgery

• Aim: overflow of air/fluid in small bowel• Ileocecal valve is usally edematous

• Complication: Perforation5 attempts, 3 mins, 3 mins breakPressure 80 -100 - 120 mm Hg

Page 53: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Pneumatic

Page 54: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Treatment

• Repositioning• Spontaneous

• Pneumatic

• Hydrostatic• Surgery

• Aim: overflow of air/fluid in small bowel• Ileocecal valve is usally edematous

• Complication: Perforation Rule of 3• 3 feet• 3 minutes• 3 times

Page 55: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Hydrostatic

Page 56: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Treatment

• Repositioning• Spontaneous

• Pneumatic

• Hydrostatic

• Surgery

• Aim: overflow of air/fluid in small bowel• Ileocecal valve is usally edematous

• Complication: Perforation

Page 57: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Key points

• Use high frequency probes

• Involve the parents

• Be aware of specific paediatric diseases

• Keep thinking!

Page 58: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK

Thank you and good luck!

Page 59: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 60: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 61: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 62: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
Page 63: BMUS Summer School 2017 Martijn Verhagen Radiologist ......BMUS Summer School 2017 Martijn Verhagen Radiologist Fellow Paediatric Radiology at GOSH, London, UK
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Malrotation and volvulus