Assesment of Hearing in Infants & Children

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    ASSESMENT OF HEARINGIN INFANTS & CHILDREN

    PRESENTED BY : DR. PRIYANJAL GAUTAMPG- 2nd Yr. (M.S. - E.N.T.)NIMS MEDICAL COLLEGE & HOSPITAL, JAIPUR

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    INTRODUCTION

    In developed countries routine screening of

    newborn child for hearing impairment is anorm.

    But in developing countries, it is usually theparents who suspect hearing impairment &bring child to the physician.

    Early diagnosis & timely intervention givesbest result in rehabilitating such children.

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    Speech & hearing are inter-related.

    For normal speech child must hears sounds.Later child understands the sounds of the

    words & intimates the words & talks.

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    CAUSES OF CONGENITALDEAFNESS

    1. Genetic defects : affects inner ear & causedeafness.

    (i) Michel aplasia : Complete failure of innerear development.

    (ii) Mondini aplasia : Cochlea has 1 turnsinstead of 2 turns.

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    Causes of permanent childhood hearingimpairment :

    (A) Congenital disorders:

    (i) Genetic- Syndromic Autosomalrecessive

    Autosomal

    dominantNonsyndromic X-linked

    Mitochondrial

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    (B) Environmental causes:

    (i) Perinatal causes: Hypoxia

    Hyperbilirubinemia

    Low birth weight

    (ii) Acquired disorders: Infections Chronicotitis media

    Meningitis

    Mumps

    AIDS

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    RISK FACTORS FORCONGENITAL HEARING LOSS

    An illness/condition requiring admission of48hrs or greater to a NICU Auditoryneuropathy/dys-synchrony.

    Stigmata associated with a syndrome knownto include a sensorineural or conductive

    hearing loss.

    Family H/O early childhood deafness.

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    TEMPORARY CHILDHOODHEARING LOSS

    Risk factors:

    Otitis media with effusion (OME)

    Passive smoking Bottle feeding

    URTI

    Admission to NICU as a newborn Day care

    Siblings having had OME

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    IDENTIFICATION OFDEAFNESS IN CHILDREN

    1. HISTORY:

    . A thorough history taking from parents ofsuspected deaf child is very important. Eg.

    H/O Attack of Measles, Herpes, Syphilis etc.to mother during early part of pregnancy isimportant.

    . Body wt. below 1.5 kg at birth, H/O drugtaken during pregnancy is important.

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    2. Normal Responses of hearing children:

    (A) Neonatal Period- Birth to 2 months

    (i) Moros Reflex: Stimulation of the sleeping

    baby with a loud sound produces startleresponse in a normal child.

    (i) Auriculo palpebral response :Stimulation of the child with loud soundproduces closure ofpalpebral fissures ina normal hearing children.

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    NEWBORN HEARING SCREENING:

    Tests used for newborn hearing screening are -:

    Automated otoacoustic emissions (AOAE)

    Transient evoked otoacoustic emissions(TEOAE)

    Distortion product otoacoustic emissions(DPOAE)

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    T i t k d i i

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    Transient-evoked emissions(TEOAEs):

    These are typicallypresented as anamplitude/timeplot of acoustic

    waveformrecorded from theear canal.

    TEOAEs greaterthan 20 db soundpressure level

    (SPL) can be

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    s or on pro uc em ss ons(DPOAEs):

    These aregenerated in thecochlea in response

    to 2 simultaneouspure-tone stimuli.

    This tonal responseis not present in the

    eliciting stimuli &therefore referredto as distortion.

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    Hearing tests in children:

    (A) Electrophysiological testing (0-6 months)

    (A) Behavioural observation audiometry (0-6

    month)

    (A) The distraction test (6-18 months)

    (A) Visual reinforcement audiometry (6-36months)

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    VISUAL REINFORCEMENTAUDIOMETRY (VRA)

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    BERA

    BERA stands for Brain Stem EvokedResponse Audiometry.

    It is an important clinical tool & morestandard parameter in the diagnosis ofhearing problems.

    It is an accurate measure of auditoryfunction & measures the electrical activity inthe auditory pathways.

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    Uses of BERA :

    1. Detection of deafness in the difficult-to-testpatients like infants, mentally retarded ormalingering subjects.

    1. Assessment of nature of deafness whetherconductive or sensory or neural.

    1. Identification of the site of lesion inretrocochlear pathologies.

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    Principle of BERA :

    v When a sound reaches cochlea, it isconverted

    into an electric impulse & passes fromcochlea

    to auditory cortex.

    P th

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    Pathway :

    Sound

    Spiral ganglion (cochlea)

    Ventral & Dorsal cochlear nuclei (brainstem)

    Superior Olivary complex (midbrain)

    Lateral Lemniscus (midbrain)

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    BERA MACHINE

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    BERA MACHINE

    ELECTRODE PLACEMENTS

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    ELECTRODE PLACEMENTSIN BERA

    1. Over the vertex orscalp (activeelectrode).

    2. Over the mastoid orearlobe of ipsilateralear (reference

    electrode).

    3. Over the forehead

    just above the nasion

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    Sound stimulus nearly 60 dB abovethreshold is given to patient via headphoneswhich deliveres a broad band click sound of

    100 micro sec. (0.1 milli sec.) duration.

    The click sound is fed into the ear to be

    tested by a headphone and the contralateralear is masked.

    A series of rapid sounds provide a stimulus& events are recorded during the 1st 10 millisec. following the sound stimulus.

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    Each of these waves represents aneuroelecritical activity generated by theneural generators at some site in the

    auditory pathway in b/w the cochlea & thebrainstem.

    WAVE SITE OF NEURALGENERATOR

    1st Cochlear Nerve (distalend)

    2nd Cochlear Nucleus

    3rd Superior Olivary

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    INTERPRETATION OF BERA RESPONSE :

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    A normal BERA recording has 5 prominentpeaks & 2 small peaks.

    These peaks are BERA potentials & sincethey have troughs & crests, they are knownas BERA waves.

    Each wave give information about a specificsegment of the auditory pathway from the

    cochlea to the brainstem region.

    Hence especially I, III, & V wave have to be

    accurately identified.

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    Wave 5th :

    It is to be identified before all the otherwaves.

    It is most reliable & easily identifiable wavein BERA tracing.

    The hallmark of 5th wave is that there is asharp negative deflection (downward)imediating following the peak.

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    Wave 4th :

    It is identified as a peak just preceding wave5th. So, once 5th wave is identified, it is notdifficult to recognize wave 4th.

    Wave 3rd :

    It is the wave preceding wave 4th. So, oncewave 4th has been recognized wave 3rd isidentified as upward peak b/w wave 2nd &4th at or beyond 3 milli sec. mark on the

    graph.

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    Wave 2nd :

    It is the peak immediately preceding thewave 3rd. This wave has a latency of appox.2 milisec. & hence it is difficult to identify.

    So, it should be looked for at or just beyond2 milisec. mark on BERA graph.

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    Wave 1st :

    It has to be recognized properly because itgive an idea whether the stimulus hascrossed over from the cochlea & the distalauditory nerve.

    If wave 1st is present & other waves 2nd,3rd, 4th & 5th are absent, it suggest that the

    stimulus has reached the cochlea wellenough but not able to proceed further. Thismeans there is retrocochlear pathology.

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    STUDY OF WAVEMORPHOLOGY

    In case of newborns the graph has 3 peaks(instead of 5 to 7 peaks in adults) & wave2nd & 4th are absent.

    Moreover the graph in newborns has a largerwave 1st & much smaller wave 5th than in

    adults.

    Note: Other pathological conditions which altersthe morphology of the graph includes- Acousticneuromas on which the time interval b/w eak

    BERA GRAPH IN

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    BERA GRAPH INACOUSTIC NEUROMA

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    BIBILOGRAPHY

    1. SCOTT BROWNS17TH EDITION,

    VOL - I

    AUDIO-VESTIBULOMETRY ANIRBAN bISWAS

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    THANK YOU !

    DR. S. P. SRIVASTAVA (Prof. & HOD)

    DR. AMIT MODWAL (Assoc. Prof.)

    DR. PRADEEP SHARMA (Assoc. Prof.)

    DR. RAKESH SABOO (Asst. Prof.)

    DR. GURLEEN KAUR (P.G. 2nd Yr.)